Author: Rahman et al. Summary: Familial Hypercholesterolemia (FH) is an autosomal dominant disorder characterized by elevated serum low-density lipoprotein cholesterol (LDL-C) levels, tendon xanthomas, and an increased risk of atherosclerotic heart disease. Diagnosing Familial Hypercholesterolemia (FH) at an early age is crucial due to its potential to lead to severe cardiovascular complications, including heart failure, joint deformities and strokes. Early detection allows for timely intervention, such as lifestyle modifications and pharmacological treatments, which can significantly reduce these risks. Case Presentations: In this case report, we present a case of FH in a 13-year-old girl residing in Faridpur, Bangladesh. The patient